Abstract

Sturge-Weber syndrome (SWS) is a rare congenital
vascular disorder characterized by facial capillary
malformation, associated capillary-venous
malformations affecting the brain and eye along
with calcification in the occipital or frontoparietal
region. Occipital and posterior parietal lobes are
the common site of involvement in SWS. Posterior
fossa involvement is a rare finding with very few
number of reported cases. Contrast enhanced MRI
is considered as the gold standard for the diagnosis
of SWS demonstrating the enhancement of pial
angioma.

Keywords: Sturge Weber Syndrome, posterior fossa